Cardiovascular Manifestations of Erdheim-Chester's Disease: A Case Series.
Arq Bras Cardiol
; 111(6): 852-855, 2018 12.
Article
en En, Pt
| MEDLINE
| ID: mdl-30517380
ABSTRACT
Erdheim-Chester Disease is a rare entity, classified as an inflammatory myeloid neoplasm, with an unknown incidence, occurring preferentially in men after 50 years of age. Classically, it has a multisystemic presentation, with the skeletal system being the most frequently affected (90% of the patients), followed by genitourinary involvement in 60% of cases and central nervous system in the pituitary and diabetes insipidus in 25% of the cases. Cardiovascular manifestations are present in more than half of the patients, with aortic infiltration and atrial pseudotumor being the most common forms.
Texto completo:
1
Bases de datos:
MEDLINE
Asunto principal:
Enfermedad de Erdheim-Chester
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Cardiopatías
Límite:
Adult
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Female
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Humans
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Male
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Middle aged
Idioma:
En
/
Pt
Revista:
Arq Bras Cardiol
Año:
2018
Tipo del documento:
Article