[A case of systemic sclerosis]. / U ne rémission « en peau de chagrin ¼.
Rev Mal Respir
; 37(4): 341-345, 2020 Apr.
Article
en Fr
| MEDLINE
| ID: mdl-32284205
ABSTRACT
In systemic sclerosis, the presence of an anti-RNA polymerase III antibody (ARNpol3) is associated with an increased risk of cancer. The characteristic picture of this serotype includes severe diffuse cutaneous involvement, a high risk of renal scleroderma crisis and a 10 year survival of only around 30%. Pulmonary involvement is less common. We report the case of a woman initially treated for drug-induced acute interstitial lung disease revealing chronic interstitial pneumonia with autoimmune features. The disease evolved in three stages with the occurrence of a rapidly progressive diffuse skin sclerosis with anti-ARNPol3 antibodies in the context of ovarian cancer remission.
Palabras clave
Texto completo:
1
Bases de datos:
MEDLINE
Asunto principal:
Neoplasias Ováricas
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Esclerodermia Sistémica
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Flecainida
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Enfermedades Pulmonares Intersticiales
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Cistadenocarcinoma Seroso
Límite:
Aged
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Female
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Humans
Idioma:
Fr
Revista:
Rev Mal Respir
Año:
2020
Tipo del documento:
Article
País de afiliación:
Francia