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TAFRO syndrome complicated by porto-sinusoidal vascular liver disease with portal hypertension: a case report.
Hayashi, Manabu; Wada, Jun; Fujita, Masashi; Asano, Tomoyuki; Matsuoka, Naoki; Fujita, Yuya; Temmoku, Jumpei; Matsumoto, Haruki; Yashio-Furuya, Makiko; Sato, Shuzo; Kobayashi, Hiroko; Watanabe, Hiroshi; Ryoichiro, Kobashi; Waragai, Yuichi; Suzuki, Erina; Kiko, Yuichiro; Abe, Kazumichi; Takahashi, Atsushi; Masuda, Tomoyuki; Hashimoto, Yuko; Migita, Kiyoshi; Ohira, Hiromasa.
Afiliación
  • Hayashi M; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan. m884884@fmu.ac.jp.
  • Wada J; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Fujita M; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Asano T; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Matsuoka N; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Fujita Y; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Temmoku J; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Matsumoto H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Yashio-Furuya M; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Sato S; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Kobayashi H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Watanabe H; Department of Rheumatology, Fukushima Medical University, Fukushima, Japan.
  • Ryoichiro K; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Waragai Y; Department of Gastroenterology, Soma General Hospital, Soma, Japan.
  • Suzuki E; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Kiko Y; Department of Gastroenterology, Soma General Hospital, Soma, Japan.
  • Abe K; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
  • Takahashi A; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
  • Masuda T; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Hashimoto Y; Department of Gastroenterology, Fukushima Medical University, 1 Hikarigaoka, Fukushima, 960-1295, Japan.
  • Migita K; Department of Pathology, School of Medicine, Iwate Medical University, Iwate, Japan.
  • Ohira H; Department of Diagnostic Pathology, Fukushima Medical University, Fukushima, Japan.
Clin J Gastroenterol ; 14(6): 1711-1717, 2021 Dec.
Article en En | MEDLINE | ID: mdl-34487333
ABSTRACT
Porto-sinusoidal vascular liver disease (PSVD) is a disorder that can cause portal hypertension without liver cirrhosis. TAFRO syndrome is a systemic inflammatory disorder with a background of immunological abnormalities. We report a case of TAFRO syndrome complicated by PSVD with portal hypertension. A 39-year-old man developed refractory ascites and esophageal varices. Lymph node histology revealed multicentric Castleman disease-like features. Intravenous methylprednisolone and tocilizumab therapy improved ascites and renal dysfunction, but the patient developed severe infections. The diagnosis of TAFRO syndrome in patients complicated by PSVD with portal hypertension encourages the consideration of appropriate treatment for these patients.
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Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Enfermedades Vasculares / Enfermedad de Castleman / Hipertensión Portal Límite: Adult / Humans / Male Idioma: En Revista: Clin J Gastroenterol Año: 2021 Tipo del documento: Article País de afiliación: Japón
Texto completo
Imprimir
XML
PubMed Links
Buscar en Google

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Enfermedades Vasculares / Enfermedad de Castleman / Hipertensión Portal Límite: Adult / Humans / Male Idioma: En Revista: Clin J Gastroenterol Año: 2021 Tipo del documento: Article País de afiliación: Japón