Management of neonatal cardiac rhabdomyoma obstructing the aortic valve.
J Card Surg
; 37(9): 2839-2841, 2022 Sep.
Article
en En
| MEDLINE
| ID: mdl-35726654
ABSTRACT
Rhabdomyomas associated with tuberous sclerosis are common cardiac tumors in children, and no surgical intervention is needed in most cases. However, when the tumor causes left ventricular outlet tract obstruction (LVOTO), immediate surgical intervention is indicated. Here, we report a newborn who was diagnosed antenatally with multiple cardiac rhabdomyomas, one of which blocked the aortic valve during systole. The tumor was resected early in the postnatal period with excellent outcomes. Until surgery, we maintained ductus arteriosus patency and systemic circulation using prostaglandin E1, which helped to reduce the risk of sudden death due to LVOTO. Postoperative two-dimensional echocardiography at discharge showed that surgery was effective in resolving LVOTO.
Palabras clave
Texto completo:
1
Bases de datos:
MEDLINE
Asunto principal:
Rabdomioma
/
Esclerosis Tuberosa
/
Neoplasias Cardíacas
Tipo de estudio:
Diagnostic_studies
Límite:
Child
/
Humans
/
Newborn
Idioma:
En
Revista:
J Card Surg
Asunto de la revista:
CARDIOLOGIA
Año:
2022
Tipo del documento:
Article
País de afiliación:
Japón