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Defective function of α-ketoglutarate dehydrogenase exacerbates mitochondrial ATP deficits during complex I deficiency.
Piroli, Gerardo G; Manuel, Allison M; McCain, Richard S; Smith, Holland H; Ozohanics, Oliver; Mellid, Sara; Cox, J Hunter; Cotham, William E; Walla, Michael D; Cascón, Alberto; Ambrus, Attila; Frizzell, Norma.
Afiliación
  • Piroli GG; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA.
  • Manuel AM; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA.
  • McCain RS; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA.
  • Smith HH; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA.
  • Ozohanics O; Department of Biochemistry, Institute of Biochemistry and Molecular Biology, Semmelweis University, Budapest, Hungary.
  • Mellid S; Hereditary Endocrine Cancer Group, Spanish National Cancer Research Centre (CNIO), 28029, Madrid, Spain.
  • Cox JH; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA.
  • Cotham WE; Mass Spectrometry Center, Department of Chemistry & Biochemistry, University of South Carolina, Columbia, SC, 29205, USA.
  • Walla MD; Mass Spectrometry Center, Department of Chemistry & Biochemistry, University of South Carolina, Columbia, SC, 29205, USA.
  • Cascón A; Hereditary Endocrine Cancer Group, Spanish National Cancer Research Centre (CNIO), 28029, Madrid, Spain; Centro de Investigación Biomédica en Red de Enfermedades Raras (CIBERER), 28029, Madrid, Spain.
  • Ambrus A; Department of Biochemistry, Institute of Biochemistry and Molecular Biology, Semmelweis University, Budapest, Hungary.
  • Frizzell N; Department of Pharmacology, Physiology & Neuroscience, School of Medicine, University of South Carolina, Columbia, SC, 29209, USA. Electronic address: norma.frizzell@uscmed.sc.edu.
Redox Biol ; 67: 102932, 2023 11.
Article en En | MEDLINE | ID: mdl-37883842

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Ciclo del Ácido Cítrico / Complejo Cetoglutarato Deshidrogenasa Límite: Animals / Humans Idioma: En Revista: Redox Biol Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos

Texto completo: 1 Bases de datos: MEDLINE Asunto principal: Ciclo del Ácido Cítrico / Complejo Cetoglutarato Deshidrogenasa Límite: Animals / Humans Idioma: En Revista: Redox Biol Año: 2023 Tipo del documento: Article País de afiliación: Estados Unidos