Vasculitis and vasculopathy associated with inborn errors of immunity: an overview.
Front Pediatr
; 11: 1258301, 2023.
Article
en En
| MEDLINE
| ID: mdl-38357265
ABSTRACT
Systemic autoinflammatory diseases (SAIDs) are disorders of innate immunity, which are characterized by unprovoked recurrent flares of systemic inflammation often characterized by fever associated with clinical manifestations mainly involving the musculoskeletal, mucocutaneous, gastrointestinal, and nervous systems. Several conditions also present with varied, sometimes prominent, involvement of the vascular system, with features of vasculitis characterized by variable target vessel involvement and organ damage. Here, we report a systematic review of vasculitis and vasculopathy associated with inborn errors of immunity.
Texto completo:
1
Bases de datos:
MEDLINE
Tipo de estudio:
Overview
/
Risk_factors_studies
Idioma:
En
Revista:
Front Pediatr
Año:
2023
Tipo del documento:
Article
País de afiliación:
Italia