RSH/SLO (Smith-Lemli-Opitz) syndrome: designing a high cholesterol diet for the SLO syndrome.
Am J Med Genet
; 50(4): 358-63, 1994 May 01.
Article
en En
| MEDLINE
| ID: mdl-8209916
ABSTRACT
A high cholesterol diet has been suggested to help prevent the poor reproductive outcomes found in heterozygote carriers of fetuses affected with the Smith-Lemli-Opitz (SLO) syndrome. The theory has also been presented that a high cholesterol medical food may enhance myelination of the central nervous system of the infant and prevent demyelination in the child and adult with SLO. Clinical studies are required to test this hypothesis and to determine the optimal composition of such medical foods. FDA requires proof of efficacy and controls nutrient composition, ingredients, and label claims of medical foods.
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Bases de datos:
MEDLINE
Asunto principal:
Anomalías Múltiples
/
Colesterol en la Dieta
/
Alimentos Fortificados
/
Colesterol
/
Enfermedades Desmielinizantes
/
Errores Innatos del Metabolismo Lipídico
Límite:
Animals
/
Female
/
Humans
/
Infant
/
Pregnancy
Idioma:
En
Revista:
Am J Med Genet
Año:
1994
Tipo del documento:
Article