[Portal hypertension and neutrocytic ascites in POEMS syndrome]. / Hypertension portale et ascite neutrocytique au cours du syndrome POEMS.

We report a case of portal hypertension and neutrocytic ascites in a 52 year old man with POEMS syndrome. POEMS syndrome is an association of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammapathy and skin changes. Portal hypertension is rare in POEMS syndrome and this is the first time that culture negative neutrocytic ascites has been described with this syndrome.

[Severity of desmoid tumors with retroperitoneal development in Gardner's syndrome. Apropos of 2 cases]. / Gravité des tumeurs desmoïdes à développement rétropéritonéal au cours du syndrome de Gardner. A propos de deux observations.

We report two cases of retroperitoneal desmoid tumours in patients with Gardner's syndrome. These tumours are rare and of poor prognosis. In our two cases, the predominant clinical manifestations were caused by compression of the ureters, bladder and nerve roots. In the first patient, the tumours developed after colectomy, while in the second patient the discovery of the desmoid tumour preceded that of a cancer of the colon. Finally, in the first patient, an attempted treatment with a non-steroidal anti-inflammatory agent (sulindac) had to be discontinued after 4 months on account of side-effects.