Detalhe da pesquisa
1.
Triple Therapy for Cystic Fibrosis Phe508del-Gating and -Residual Function Genotypes.
N Engl J Med
; 385(9): 815-825, 2021 08 26.
Artigo
em Inglês
| MEDLINE | ID: mdl-34437784
2.
Long-term safety and efficacy of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis and at least one F508del allele: 144-week interim results from a 192-week open-label extension study.
Eur Respir J
; 62(6)2023 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-37945033
3.
Genetic therapies in cystic fibrosis.
Curr Opin Pulm Med
; 29(6): 615-620, 2023 11 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-37700667
4.
Cystic fibrosis.
Lancet
; 397(10290): 2195-2211, 2021 06 05.
Artigo
em Inglês
| MEDLINE | ID: mdl-34090606
5.
Elexacaftor-Tezacaftor-Ivacaftor for Cystic Fibrosis with a Single Phe508del Allele.
N Engl J Med
; 381(19): 1809-1819, 2019 11 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-31697873
6.
Genetic association and transcriptome integration identify contributing genes and tissues at cystic fibrosis modifier loci.
PLoS Genet
; 15(2): e1008007, 2019 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-30807572
7.
Losartan Rescues Inflammation-related Mucociliary Dysfunction in Relevant Models of Cystic Fibrosis.
Am J Respir Crit Care Med
; 201(3): 313-324, 2020 02 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-31613648
8.
Triple Therapy for Cystic Fibrosis Phe508del-Gating and -Residual Function Genotypes. Reply.
N Engl J Med
; 385(23): 2208, 2021 12 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-34874646
9.
Airway Mucosal Host Defense Is Key to Genomic Regulation of Cystic Fibrosis Lung Disease Severity.
Am J Respir Crit Care Med
; 197(1): 79-93, 2018 01 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-28853905
10.
Diagnosis of Primary Ciliary Dyskinesia. An Official American Thoracic Society Clinical Practice Guideline.
Am J Respir Crit Care Med
; 197(12): e24-e39, 2018 06 15.
Artigo
em Inglês
| MEDLINE | ID: mdl-29905515
11.
Chasing Zero: Increasing Infection Control Compliance on an Inpatient Cystic Fibrosis Unit.
J Nurs Care Qual
; 33(1): 67-71, 2018.
Artigo
em Inglês
| MEDLINE | ID: mdl-28658183
12.
Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor for 24 Weeks or Longer in People with Cystic Fibrosis and One or More F508del Alleles: Interim Results of an Open-Label Phase 3 Clinical Trial.
Am J Respir Crit Care Med
; 203(3): 381-385, 2021 02 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-32969708
13.
Treatment recommendations in Primary Ciliary Dyskinesia.
Paediatr Respir Rev
; 18: 39-45, 2016 Mar.
Artigo
em Inglês
| MEDLINE | ID: mdl-26586601
14.
Effect of extracorporeal photopheresis on lung function decline for severe bronchiolitis obliterans syndrome following allogeneic stem cell transplantation.
J Clin Apher
; 31(4): 347-52, 2016 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-26031713
15.
Unraveling the CFTR Function-Phenotype Connection for Precision Treatment in Cystic Fibrosis.
Am J Respir Crit Care Med
; 199(9): 1053-1054, 2019 May 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-30939246
16.
Gilbert's syndrome leads to elevated bilirubin after initiation of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis.
Pediatr Pulmonol
; 59(4): 863-866, 2024 Apr.
Artigo
em Inglês
| MEDLINE | ID: mdl-38179880
17.
Safety of non-cuffed tunneled central venous catheters in adults with cystic fibrosis.
Respir Med Res
; 85: 101073, 2023 Nov 30.
Artigo
em Inglês
| MEDLINE | ID: mdl-38157768
18.
Sex and Gender in Lung Diseases and Sleep Disorders: A State-of-the-Art Review: Part 2.
Chest
; 163(2): 366-382, 2023 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-36183784
19.
Partners in research: The success with therapies research consortium and the CF community unite to improve self-management.
J Cyst Fibros
; 22(5): 830-835, 2023 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-37137747
20.
Complications and Practice Variation in the Use of Peripherally Inserted Central Venous Catheters in People With Cystic Fibrosis: The Prospective Study of Peripherally Inserted Venous Catheters in People With Cystic Fibrosis Study.
Chest
; 164(3): 614-624, 2023 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-37019356