RESUMO
Cardiac papillary fibroelastomas are rare benign tumors of the heart with potential for life-threatening complications. The incidence of multiple lesions is less than 10% of all reported cases. Preoperative transesophageal echocardiography is important for detecting all cardiac sites involving this tumor, because excision of all such tumors must be performed to prevent serious complications. Here, the first ever case is reported of multiple infected papillary fibroelastoma of the mitral valve, aortic valve and left ventricular outflow tract with massive mitral insufficiency in a patient with hypertrophic cardiomyopathy.
Assuntos
Cardiomiopatia Hipertrófica/complicações , Endocardite Bacteriana/complicações , Fibroma/complicações , Neoplasias Cardíacas/complicações , Infecções Estafilocócicas/complicações , Adulto , Cardiomiopatia Hipertrófica/diagnóstico , Ecocardiografia Transesofagiana , Endocardite Bacteriana/diagnóstico , Fibroma/diagnóstico , Neoplasias Cardíacas/diagnóstico , Humanos , Masculino , Infecções Estafilocócicas/diagnósticoRESUMO
Idiopathic hypereosinophilic syndrome is a rare systemic disease than can cause multiple organ failure by eosinophilic infiltration. Cardiac involvement is characterized by endocardial fibrosis and overlying thrombus, leading to restrictive cardiomyopathy and valvular dysfunction. Surgical experience of patients with mitral dysfunction caused by this syndrome is limited, and valvular replacement is most often performed. Mechanical valvular replacement has a high incidence of recurrent obstructive thrombosis, and replacement with a bioprosthesis is recommended, despite associated restrictive cardiomyopathy. A patient is described who presented with mitral insufficiency associated with idiopathic hypereosinophilic syndrome, and underwent mitral valve repair.
Assuntos
Bioprótese , Próteses Valvulares Cardíacas , Síndrome Hipereosinofílica/complicações , Insuficiência da Valva Mitral/cirurgia , Idoso , Humanos , Masculino , Valva Mitral/cirurgia , Insuficiência da Valva Mitral/etiologiaRESUMO
Idiopathic hypereosinophilic syndrome (IHS) is a rare systemic disease than can cause multiple organ failure by eosinophilic infiltration. Cardiac involvement is characterized by endocardial fibrosis and overlying thrombus leading to restrictive cardiomyopathy and valvular dysfunction. The absence of peripheral eosinophilia does not exclude eosinophilic cardiac involvement. Surgical experience of patients with mitral dysfunction caused by this syndrome is limited and valvular replacement is most often performed. Mechanical valvular replacement has a high incidence of recurrent obstructive thrombosis and replacement by bioprosthesis is recommended despite associated restrictive cardiomyopathy. This report describes a patient who presented mitral insufficiency caused by eosinophilic endocarditis without peripheral eosinophilia who underwent mitral valve replacement.