RESUMO
A thrombocytopenic patient with pulmonary hemangiolymphangiectasia proven by biopsy, was studied for platelet sequestration with In-111-labeled autologous platelets. The 24-hour scan showed diffuse increased uptake throughout both lung fields, indicating platelet sequestration by the diffuse pulmonary hemangiolymphangiectasia.
Assuntos
Plaquetas/diagnóstico por imagem , Hemangioma/sangue , Índio , Neoplasias Pulmonares/sangue , Linfangiectasia/sangue , Radioisótopos , Criança , Feminino , Hemangioma/diagnóstico por imagem , Humanos , Neoplasias Pulmonares/diagnóstico por imagem , Linfangiectasia/diagnóstico por imagem , CintilografiaRESUMO
Renal lymphangiectasia is a rare disorder characterized by dilatation of peripelvic, renal and perirenal lymphatic ducts. The exact etiology is not known. Congenital forms and ac-quired forms have been described. The latter has been attributed to obstruction of draining retro-peritoneal lymphatic ducts caused by either infection, inflammation or any other cause. We des-cribe the rare association of renal lymphangiectasia with chronic myeloid leukemia, which is probably not yet reported in the medical literature.
Assuntos
Nefropatias/etiologia , Leucemia Mielogênica Crônica BCR-ABL Positiva/complicações , Linfangiectasia/etiologia , Contagem de Células Sanguíneas , Humanos , Rim/fisiopatologia , Nefropatias/sangue , Linfangiectasia/sangue , Anormalidades Linfáticas/sangue , Sistema Linfático/fisiopatologia , Masculino , Pessoa de Meia-IdadeRESUMO
Lymphangiectasia is a congenital or acquired disorder characterized by abnormal, dilated lymphatics with a variable age of presentation. We describe a case of lymphangiectasia with intestinal and pulmonary involvement in an adolescent female, who presented with many of the classic features including chylous pleural effusions, lymphopenia, hypogammaglobinemia, and a protein-losing enteropathy. She also presented with recurrent lower gastrointestinal bleeding, which is infrequently described. The patient did not improve with bowel rest and a low-fat medium-chain triglyceride diet and had little improvement with octreotide acetate therapy. However, she had a clinical response to antiplasmin therapy, trans-4-aminothylcyclohexamine carboxylic acid (tranexamic acid) in terms of serum albumin and gastrointestinal bleeding. She continues to have exacerbations of her condition, as well as persistent lymphopenia and chronic pleural effusions.