RESUMO
Eccrine nevus (EN) is a very rare hamartoma of the skin and with varying clinical manifestations. Histologically, these neoplasms present as a proliferation of normally structured eccrine sweat glands in the dermis. There have been no more than 20 cases previously have been reported in the English literature. Herein we report a 25-year-old man with eccrine nevus on the neck. To our best knowledge, this is the first case that the lesion affecting the neck.
Assuntos
Glândulas Écrinas , Nevo/congênito , Neoplasias Cutâneas/congênito , Neoplasias das Glândulas Sudoríparas/congênito , Adulto , Glândulas Écrinas/patologia , Humanos , Masculino , Pescoço/patologia , Nevo/patologia , Neoplasias Cutâneas/patologia , Neoplasias das Glândulas Sudoríparas/patologiaRESUMO
Syringocystadenocarcinoma papilliferum (SCACP) is a rare adenexal carcinoma with only 21 cases reported in the literature. Most patients describe a long-standing mass with recent change, supporting the idea that SCACP arises from malignant transformation of pre-existing syringocystadenoma papilliferum (SCAP). Syringocystadenocarcinoma papilliferum is generally treated with wide surgical excision of the lesion and patients do exceeding well and require no systemic therapy.
Assuntos
Cistadenocarcinoma/diagnóstico , Neoplasias de Cabeça e Pescoço/diagnóstico , Couro Cabeludo/patologia , Neoplasias das Glândulas Sudoríparas/diagnóstico , Adenoma de Glândula Sudorípara/congênito , Adenoma de Glândula Sudorípara/patologia , Idoso , Cistadenocarcinoma/patologia , Cistadenocarcinoma/cirurgia , Progressão da Doença , Neoplasias de Cabeça e Pescoço/congênito , Neoplasias de Cabeça e Pescoço/patologia , Neoplasias de Cabeça e Pescoço/cirurgia , Humanos , Masculino , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologia , Neoplasias das Glândulas Sudoríparas/cirurgiaRESUMO
Microcystic adenexal carcinoma is a rare, locally aggressive, malignant appendage tumor also known as sclerosing sweat duct carcinoma. Since widespread recognition of microcystic adenexal carcinoma as a distinct clinicopathologic entity, approximately 300 total cases have been reported in the literature, with only eight previous cases reported in children under the age of 18, with no reported cases in patients younger than 6 years old. Our patient is unique in that the lesion was present at birth, making this the youngest case of microcystic adenexal carcinoma reported.
Assuntos
Carcinoma de Apêndice Cutâneo/congênito , Carcinoma de Apêndice Cutâneo/patologia , Bochecha/patologia , Neoplasias Faciais/congênito , Neoplasias Faciais/patologia , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologia , Carcinoma de Apêndice Cutâneo/cirurgia , Neoplasias Faciais/cirurgia , Feminino , Humanos , Recém-Nascido , Neoplasias das Glândulas Sudoríparas/cirurgia , Resultado do TratamentoRESUMO
Eccrine spiradenoma (ES) is a benign uncommon tumor of skin adnexa with a characteristic clinical and histopathological presentation. Typically, it presents as a painful, slow growing and solitary nodule on the head or upper trunk in adult patients. We report a child with linear ES which presented with asymptomatic papulonodular lesions in a blaschkoid distribution on the face. Cases reported in the literature of multiple spiradenomas are very rare and multiple linear lesions are even rarer. To date, 21 cases of linear/multiple ES have been reported. Of these, eight were in children or adolescents. We report an additional case of this rare clinical presentation and review the literature.
Assuntos
Adenoma de Glândula Sudorípara/congênito , Glândulas Écrinas/patologia , Neoplasias Primárias Múltiplas/congênito , Neoplasias das Glândulas Sudoríparas/congênito , Adenoma de Glândula Sudorípara/patologia , Criança , Feminino , Humanos , Neoplasias Primárias Múltiplas/patologia , Neoplasias das Glândulas Sudoríparas/patologiaRESUMO
Eccrine angiomatous hamartoma is a rare entity characterized histologically by the combination of proliferative eccrine and vascular elements. It generally arises before puberty, as solitary or multiple lesions, with a heterogeneous clinical appearance, affecting predominantly the distal extremities, with or without associated pain or hyperhidrosis. It may require surgical treatment due to cosmetic concern, progressive enlargement or the presence of pain or excessive hyperhidrosis. We report five congenital cases of eccrine angiomatous hamartoma, emphasizing a clinically uncommon tumor-like appearance, with numerous telangiectasias on their surfaces resembling vascular lesions, in two of them.
Assuntos
Glândulas Écrinas/patologia , Hamartoma/congênito , Doenças das Glândulas Sudoríparas/congênito , Feminino , Hamartoma/patologia , Humanos , Lactente , Masculino , Doenças das Glândulas Sudoríparas/patologia , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologiaAssuntos
Axila/patologia , Hidrocistoma/diagnóstico , Neoplasias das Glândulas Sudoríparas/diagnóstico , Biópsia , Diagnóstico Diferencial , Hidrocistoma/congênito , Hidrocistoma/patologia , Humanos , Lactente , Masculino , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologiaRESUMO
We present a 5-month-old girl with one localized plaque in a bandlike distribution on the left wrist since birth. Localized hyperhidrosis was also noted. Histopathologic examination of the lesion showed typical findings of mucinous eccrine nevus. Our report may serve to alert dermatologists to consider this entity in congenital lesions.
Assuntos
Dermatite/patologia , Glândulas Écrinas/patologia , Nevo/patologia , Neoplasias das Glândulas Sudoríparas/patologia , Biópsia , Glândulas Écrinas/anormalidades , Feminino , Humanos , Hiperidrose/congênito , Hiperidrose/patologia , Lactente , Mucinas , Nevo/congênito , Neoplasias das Glândulas Sudoríparas/congênitoRESUMO
We present a boy with a congenital, ulcerated nodule on the scalp. At birth, the lesion was considered to be the result of a traumatic injury, but a biopsy at the age of 6 months pointed to a diagnosis of syringocystadenoma papilliferum. We draw attention to the difficulty of identifying head lesions in young children from clinical signs alone.
Assuntos
Adenoma de Glândula Sudorípara/congênito , Adenoma de Glândula Sudorípara/patologia , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologia , Adenoma de Glândula Sudorípara/cirurgia , Biópsia por Agulha , Seguimentos , Humanos , Imuno-Histoquímica , Lactente , Masculino , Fatores de Risco , Couro Cabeludo , Neoplasias das Glândulas Sudoríparas/cirurgia , Resultado do TratamentoRESUMO
We report a rare congenital scalp tumour with histological diagnosis of a congenital apocrine adenoma with features of a tubular adenoma. Following cranial CT and MRI, the tumour was serially excised. The macroscopic and microscopic appearances and management are discussed. To our knowledge, such a case has not been previously reported.
Assuntos
Glândulas Apócrinas , Neoplasias de Cabeça e Pescoço/congênito , Couro Cabeludo , Neoplasias Cutâneas/congênito , Neoplasias das Glândulas Sudoríparas/congênito , Feminino , Neoplasias de Cabeça e Pescoço/patologia , Neoplasias de Cabeça e Pescoço/cirurgia , Humanos , Recém-Nascido , Neoplasias Cutâneas/patologia , Neoplasias Cutâneas/cirurgia , Neoplasias das Glândulas Sudoríparas/patologia , Neoplasias das Glândulas Sudoríparas/cirurgiaAssuntos
Cistadenoma/congênito , Neoplasias das Glândulas Sudoríparas/congênito , Adulto , Biópsia , Cistadenoma/diagnóstico , Cistadenoma/patologia , Cistadenoma/cirurgia , Progressão da Doença , Feminino , Humanos , Pele/patologia , Esterno , Neoplasias das Glândulas Sudoríparas/diagnóstico , Neoplasias das Glândulas Sudoríparas/patologia , Neoplasias das Glândulas Sudoríparas/cirurgia , Glândulas Sudoríparas/patologiaRESUMO
Eccrine spiradenoma is an uncommon tumour of the sweat gland(s) and generally occurs as a solitary small painful nodule. Very rarely, it may present as multiple tumours arranged in a linear/blaschkoid pattern. An 8-year-old girl had many papulonodular lesions, arranged in a linear pattern on the left half of the face, involving the forehead and lateral side of the nose. The lesions were along Blaschko's lines. Lesions were reported to be present at birth; no family member had similar lesion(s), either in solitary or multiple form. Histopathologic examination of a biopsy specimen revealed characteristic features of eccrine spiradenoma. The case is reported because of the rare occurrence of this presentation.
Assuntos
Adenoma de Glândula Sudorípara/congênito , Glândulas Écrinas/patologia , Face , Neoplasias das Glândulas Sudoríparas/congênito , Adenoma de Glândula Sudorípara/patologia , Biópsia , Criança , Feminino , Humanos , Neoplasias das Glândulas Sudoríparas/patologiaAssuntos
Couro Cabeludo/patologia , Neoplasias das Glândulas Sudoríparas/congênito , Neoplasias das Glândulas Sudoríparas/patologia , Adenomas Tubulares de Glândulas Sudoríparas/congênito , Adenomas Tubulares de Glândulas Sudoríparas/patologia , Humanos , Recém-Nascido , Masculino , Couro Cabeludo/cirurgiaRESUMO
A 6-year-old girl with congenital porokeratotic eccrine ostial and dermal duct nevus involving the palmoplantar surfaces (ie, the back of the hands and feet), the limbs, the neck, and the axillae is described. The clinical and histopathologic findings are presented. This entity should be taken into consideration in the differential diagnosis of linear keratotic cutaneous eruptions.
Assuntos
Ceratose/patologia , Nevo Pigmentado/patologia , Neoplasias das Glândulas Sudoríparas/patologia , Criança , Diagnóstico Diferencial , Glândulas Écrinas/patologia , Feminino , Humanos , Ceratose/congênito , Nevo Pigmentado/congênito , Paraceratose/patologia , Neoplasias das Glândulas Sudoríparas/congênitoRESUMO
This is the case of a 13 year-old female evaluated for a congenital skin lesion on the left buttock. Physical examination revealed a well-defined light brown patch with a 4mm papule on the center. A skin biopsy revealed an increased number of eccrine glands associated to a proliferation of vascular channels, particularly capillaries. These findings are consistent with a diagnosis of eccrine angiomatous hamartoma.