Moyamoya disease: report of three cases in Brazilian patients
Arq. neuropsiquiatr
; Arq. neuropsiquiatr;57(2B): 371-6, jun. 1999. tab, ilus
Article
em En
| LILACS
| ID: lil-236062
Biblioteca responsável:
BR1.1
RESUMO
Moyamoya disease (MMD) is a chronic occlusive cerebrovascular disease of unknown etiology reported mainly in the Japanese. Most cases occur in children. The disease is rare in non-Oriental adults manifesting itself mostly as intracerebral hemorrhages. We describe MMD in 2 non-Oriental young adults and one adolescent that developed cerebral infarctions. The adults were medicated with aspirin and no medication was given to the adolescent. All patients did not deteriorate in a follow-up period from 1 to 4 years. Although rare, MMD is na important cause of stroke in young individuals and may well be underreported only 18 patients have been reported till 1997 in Brazil. Neurologists should include MMD in differential diagnosis of ischemic and hemorrhagic strokes in young adults.
Texto completo:
1
Base de dados:
LILACS
Assunto principal:
Doença de Moyamoya
Tipo de estudo:
Observational_studies
/
Prognostic_studies
Limite:
Adolescent
/
Adult
/
Humans
/
Male
País/Região como assunto:
America do sul
/
Brasil
Idioma:
En
Revista:
Arq Neuropsiquiatr
/
Arq. neuropsiquiatr
/
Arq. neuropsiquiatr. (Online)
/
Arquivos de neuro-psiquiatria (Impresso)
Assunto da revista:
NEUROLOGIA
/
PSIQUIATRIA
Ano de publicação:
1999
Tipo de documento:
Article