[Proliferation of the transverse tubular system during a tardive and familial myopathy]. / Prolifération du système tubulaire transversal au cours d'une myopathie tardive et familiale

ABSTRACT

The authors report a case of non-progressive, late-onset, recessive, sex-linked myopathy. Electron microscopy reveals a striking proliferation of the T system. This proliferation might be interpreted as indicating an abortive attempt of muscle to regenerate, which could explain the clinical course. Some basic ultrastructural aspects concerning the T system are reported. The signification of the findings of numerous "zebra bodies" is discussed.