Postnatal management of congenital bilateral renal hypodysplasia.
J Matern Fetal Neonatal Med
; 23 Suppl 3: 97-100, 2010 Oct.
Article
em En
| MEDLINE
| ID: mdl-20828237
Renal hypodysplasia (RHD) is a congenital disorder, characterized by an abnormally developed kidney. Mutations in genes such as PAX2, HNF1-beta, TCF2, EYA1, that encode factors critical in early renal development, are being found. RHD is the leading cause of chronic renal failure in childhood, with or without associated urologic abnormalities such as vesicoureteric reflux and urinary tract obstruction. Antenatal detection has improved understanding of this disorder, resulting in enhanced outcomes through earlier intervention, including peritoneal dialysis. Management requires a multidisciplinary team approach that commences prior to the birth of the child.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Doenças do Recém-Nascido
/
Rim
/
Nefropatias
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Prognostic_studies
Limite:
Humans
/
Newborn
Idioma:
En
Revista:
J Matern Fetal Neonatal Med
Assunto da revista:
OBSTETRICIA
/
PERINATOLOGIA
Ano de publicação:
2010
Tipo de documento:
Article
País de afiliação:
Itália