Multicentric infantile hemangiopericytoma: case report and review of the literature.
J Pediatr Hematol Oncol
; 33(4): e166-70, 2011 May.
Article
em En
| MEDLINE
| ID: mdl-21516017
ABSTRACT
Hemangiopericytomas are rare tumors in which outcome varies with age of onset. Those developing in adults and older children tend to be aggressive with a poor prognosis. However, infantile hemangiopericytomas often behave in a more benign manner. Recent findings suggest aggressive lesions may be histogenetically distinct. Multicentric disease is exceptionally rare, but tends to occur in infants and poses a therapeutic challenge. We present a case with extensive cutaneous and intracranial involvement, which resolved spontaneously. Tumor behavior is a key consideration in management, with careful observation recommended in uncomplicated cases and intervention indicated if more aggressive growth or spread occurs.
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Neoplasias Cutâneas
/
Neoplasias Encefálicas
/
Hemangiopericitoma
/
Neoplasias Primárias Múltiplas
Tipo de estudo:
Prognostic_studies
Limite:
Child
/
Humans
/
Male
Idioma:
En
Revista:
J Pediatr Hematol Oncol
Assunto da revista:
HEMATOLOGIA
/
NEOPLASIAS
/
PEDIATRIA
Ano de publicação:
2011
Tipo de documento:
Article
País de afiliação:
Estados Unidos