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Neuroinflammation, mitochondrial defects and neurodegeneration in mucopolysaccharidosis III type C mouse model.
Martins, Carla; Hulková, Helena; Dridi, Larbi; Dormoy-Raclet, Virginie; Grigoryeva, Lubov; Choi, Yoo; Langford-Smith, Alexander; Wilkinson, Fiona L; Ohmi, Kazuhiro; DiCristo, Graziella; Hamel, Edith; Ausseil, Jerôme; Cheillan, David; Moreau, Alain; Svobodová, Eva; Hájková, Zuzana; Tesarová, Markéta; Hansíková, Hana; Bigger, Brian W; Hrebícek, Martin; Pshezhetsky, Alexey V.
Afiliação
  • Martins C; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Hulková H; 2 Institute of Inherited Metabolic Disorders, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Dridi L; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Dormoy-Raclet V; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Grigoryeva L; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Choi Y; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Langford-Smith A; 3 Stem Cell and Neurotherapies, University of Manchester, Manchester, UK.
  • Wilkinson FL; 3 Stem Cell and Neurotherapies, University of Manchester, Manchester, UK.
  • Ohmi K; 4 Department of Biological Chemistry, David Geffen School of Medicine, University of California Los Angeles, Los Angeles, California, USA.
  • DiCristo G; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Hamel E; 5 Montreal Neurological Institute, McGill University, Montréal, QC, Canada.
  • Ausseil J; 6 CHU Amiens, and Unité INSERM U1088, UFR de Médecine, Université de Picardie-Jules Verne, Amiens, France.
  • Cheillan D; 7 Service des Maladies Héréditaires du Métabolisme et Dépistage Néonatal - Centre de Biologie Est, Hospices Civils de Lyon, Bron, France.
  • Moreau A; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada.
  • Svobodová E; 2 Institute of Inherited Metabolic Disorders, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Hájková Z; 8 Department of Paediatrics, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Tesarová M; 8 Department of Paediatrics, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Hansíková H; 8 Department of Paediatrics, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Bigger BW; 3 Stem Cell and Neurotherapies, University of Manchester, Manchester, UK.
  • Hrebícek M; 2 Institute of Inherited Metabolic Disorders, First Faculty of Medicine and General University Hospital in Prague, Charles University, Prague, Czech Republic.
  • Pshezhetsky AV; 1 CHU Ste-Justine, University of Montreal, Montreal, QC, Canada alexei.pchejetski@umontreal.ca.
Brain ; 138(Pt 2): 336-55, 2015 Feb.
Article em En | MEDLINE | ID: mdl-25567323

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Mucopolissacaridose III / Doenças Neurodegenerativas / Doenças Mitocondriais / Neurite (Inflamação) Tipo de estudo: Etiology_studies Limite: Animals Idioma: En Revista: Brain Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Canadá

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Mucopolissacaridose III / Doenças Neurodegenerativas / Doenças Mitocondriais / Neurite (Inflamação) Tipo de estudo: Etiology_studies Limite: Animals Idioma: En Revista: Brain Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Canadá