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Poly(GR) impairs protein translation and stress granule dynamics in C9orf72-associated frontotemporal dementia and amyotrophic lateral sclerosis.
Zhang, Yong-Jie; Gendron, Tania F; Ebbert, Mark T W; O'Raw, Aliesha D; Yue, Mei; Jansen-West, Karen; Zhang, Xu; Prudencio, Mercedes; Chew, Jeannie; Cook, Casey N; Daughrity, Lillian M; Tong, Jimei; Song, Yuping; Pickles, Sarah R; Castanedes-Casey, Monica; Kurti, Aishe; Rademakers, Rosa; Oskarsson, Bjorn; Dickson, Dennis W; Hu, Wenqian; Gitler, Aaron D; Fryer, John D; Petrucelli, Leonard.
Afiliação
  • Zhang YJ; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Gendron TF; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
  • Ebbert MTW; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • O'Raw AD; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
  • Yue M; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Jansen-West K; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Zhang X; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Prudencio M; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Chew J; Department of Biochemistry and Molecular Biology, Mayo Clinic, Rochester, MN, USA.
  • Cook CN; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Daughrity LM; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
  • Tong J; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Song Y; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
  • Pickles SR; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Castanedes-Casey M; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
  • Kurti A; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Rademakers R; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Oskarsson B; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Dickson DW; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Hu W; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Gitler AD; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Fryer JD; Department of Neuroscience, Mayo Clinic, Jacksonville, FL, USA.
  • Petrucelli L; Neurobiology of Disease Graduate Program, Mayo Graduate School, Mayo Clinic College of Medicine, Rochester, MN, USA.
Nat Med ; 24(8): 1136-1142, 2018 08.
Article em En | MEDLINE | ID: mdl-29942091

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Estresse Fisiológico / Biossíntese de Proteínas / Grânulos Citoplasmáticos / Dipeptídeos / Demência Frontotemporal / Proteína C9orf72 / Esclerose Lateral Amiotrófica Tipo de estudo: Prognostic_studies / Risk_factors_studies Limite: Animals / Humans Idioma: En Revista: Nat Med Assunto da revista: BIOLOGIA MOLECULAR / MEDICINA Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Estados Unidos

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Estresse Fisiológico / Biossíntese de Proteínas / Grânulos Citoplasmáticos / Dipeptídeos / Demência Frontotemporal / Proteína C9orf72 / Esclerose Lateral Amiotrófica Tipo de estudo: Prognostic_studies / Risk_factors_studies Limite: Animals / Humans Idioma: En Revista: Nat Med Assunto da revista: BIOLOGIA MOLECULAR / MEDICINA Ano de publicação: 2018 Tipo de documento: Article País de afiliação: Estados Unidos