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The role of an accurate diagnosis of inherited thrombocytopenia as the basis for an effective treatment. A case of MYH9 syndrome treated with a TPO-RA.
Porrazzo, Marika; Baldacci, Erminia; Ferretti, Antonietta; Miulli, Eleonora; Chistolini, Antonio; Pecci, Alessandro; Mazzucconi, Maria Gabriella; Foà, Robin; Santoro, Cristina.
Afiliação
  • Porrazzo M; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Baldacci E; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Ferretti A; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Miulli E; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Chistolini A; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Pecci A; Department of Internal Medicine, IRCCS Policlinico San Matteo Foundation and University of Pavia, Pavia, Italy.
  • Mazzucconi MG; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Foà R; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
  • Santoro C; Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.
Haemophilia ; 25(4): e288-e290, 2019 Jul.
Article em En | MEDLINE | ID: mdl-30993846

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Trombocitopenia / Cadeias Pesadas de Miosina / Receptores de Trombopoetina / Mutação Tipo de estudo: Diagnostic_studies Limite: Female / Humans / Middle aged Idioma: En Revista: Haemophilia Assunto da revista: HEMATOLOGIA Ano de publicação: 2019 Tipo de documento: Article País de afiliação: Itália

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Trombocitopenia / Cadeias Pesadas de Miosina / Receptores de Trombopoetina / Mutação Tipo de estudo: Diagnostic_studies Limite: Female / Humans / Middle aged Idioma: En Revista: Haemophilia Assunto da revista: HEMATOLOGIA Ano de publicação: 2019 Tipo de documento: Article País de afiliação: Itália