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Fatal Acute Exacerbation of Familial Interstitial Pneumonia Complicated with Dyskeratosis Congenita after Influenza Virus B Infection.
Tachiwada, Takashi; Oda, Keishi; Tahara, Masahiro; Sennari, Konomi; Nemoto, Kazuki; Noguchi, Shingo; Kawanami, Toshinori; Kido, Takashi; Yamaguchi, Hiroki; Yatera, Kazuhiro.
Afiliação
  • Tachiwada T; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Oda K; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Tahara M; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Sennari K; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Nemoto K; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Noguchi S; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Kawanami T; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Kido T; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
  • Yamaguchi H; Department of Hematology, Nippon Medical School, Japan.
  • Yatera K; Department of Respiratory Medicine, University of Occupational and Environmental Health, Japan.
Intern Med ; 58(18): 2683-2687, 2019 Sep 15.
Article em En | MEDLINE | ID: mdl-31178485
ABSTRACT
Dyskeratosis congenita (DC) is occasionally complicated in patients with familial interstitial pneumonia (FIP). However, there have been no reports of FIP patients with DC that develop acute exacerbation (AE). We herein report a FIP patient with DC that showed AE of FIP after influenza virus B infection. Although DC is a rare disease in clinical practice, physicians should keep in mind that FIP combined with DC has the potential to cause AE.
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Texto completo: 1 Base de dados: MEDLINE Assunto principal: Doenças Pulmonares Intersticiais / Disceratose Congênita / Influenza Humana Limite: Adult / Humans / Male Idioma: En Revista: Intern Med Assunto da revista: MEDICINA INTERNA Ano de publicação: 2019 Tipo de documento: Article País de afiliação: Japão

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Doenças Pulmonares Intersticiais / Disceratose Congênita / Influenza Humana Limite: Adult / Humans / Male Idioma: En Revista: Intern Med Assunto da revista: MEDICINA INTERNA Ano de publicação: 2019 Tipo de documento: Article País de afiliação: Japão