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Impairment of Proteasome and Autophagy Underlying the Pathogenesis of Leukodystrophy.
Lin, Dar-Shong; Ho, Che-Sheng; Huang, Yu-Wen; Wu, Tsu-Yen; Lee, Tsung-Han; Huang, Zo-Darr; Wang, Tuan-Jen; Yang, Shun-Jie; Chiang, Ming-Fu.
Afiliação
  • Lin DS; Department of Pediatrics, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Ho CS; Department of Medicine and Institute of Biomedical Sciences, Mackay Medical College, New Taipei 25245, Taiwan.
  • Huang YW; Department of Pediatric Neurology, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Wu TY; Department of Medical Research, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Lee TH; Department of Medical Research, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Huang ZD; Department of Medical Research, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Wang TJ; Department of Medical Research, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Yang SJ; Department of Laboratory Medicine, Mackay Memorial Hospital, Taipei 10449, Taiwan.
  • Chiang MF; Department of Medical Research, Mackay Memorial Hospital, Taipei 10449, Taiwan.
Cells ; 9(5)2020 05 01.
Article em En | MEDLINE | ID: mdl-32370022

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Autofagia / Complexo de Endopeptidases do Proteassoma / Leucodistrofia de Células Globoides Tipo de estudo: Etiology_studies / Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Cells Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Taiwan

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Autofagia / Complexo de Endopeptidases do Proteassoma / Leucodistrofia de Células Globoides Tipo de estudo: Etiology_studies / Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Cells Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Taiwan