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Longitudinal Outcomes in Young Patients with Alpha-1-Antitrypsin Deficiency with Native Liver Reveal that Neonatal Cholestasis is a Poor Predictor of Future Portal Hypertension.
Teckman, Jeffrey; Rosenthal, Philip; Hawthorne, Kieran; Spino, Cathie; Bass, Lee M; Murray, Karen F; Kerkar, Nanda; Magee, John C; Karpen, Saul; Heubi, James E; Molleston, Jean P; Squires, Robert H; Kamath, Binita M; Guthery, Stephen L; Loomes, Kathleen M; Sherker, Averell H; Sokol, Ronald J.
Afiliação
  • Teckman J; Pediatrics and Biochemistry, Saint Louis University, Cardinal Glennon Children's Medical Center, Saint Louis, MO.
  • Rosenthal P; Pediatrics and Surgery, University of California San Francisco, San Francisco, CA.
  • Hawthorne K; Arbor Research Collaborative for Health, Ann Arbor, MI.
  • Spino C; Biostatistics, University of Michigan, Ann Arbor, MI.
  • Bass LM; Pediatrics, Northwestern University Feinberg School of Medicine, Chicago, IL.
  • Murray KF; Pediatric Gastroenterology and Hepatology, Seattle Children's Hospital, University of Washington School of Medicine, Seattle, WA.
  • Kerkar N; Pediatric Gastroenterology, Children's Hospital Los Angeles, Los Angeles, CA.
  • Magee JC; Surgery, University of Michigan School of Medicine, Ann Arbor, MI.
  • Karpen S; Pediatrics, Emory University, Children's Healthcare Atlanta, Atlanta, GA.
  • Heubi JE; Pediatric Gastroenterology and Hepatology, Children's Hospital Medical Center, Cincinnati, OH.
  • Molleston JP; Pediatric Gastroenterology, Hepatology and Nutrition, James Whitcomb Riley Hospital for Children, Indianapolis, IN.
  • Squires RH; Pediatrics, University of Pittsburgh, Pittsburgh, PA.
  • Kamath BM; Pediatric Gastroenterology, Hepatology and Nutrition, The Hospital for Sick Children, Toronto, Ontario, Canada.
  • Guthery SL; Department of Pediatrics, Division of Gastroenterology, Hepatology and Nutrition, University of Utah, and Intermountain Primary Children's Hospital, Salt Lake City, UT.
  • Loomes KM; Pediatric Gastroenterology, Children's Hospital of Philadelphia, Philadelphia, PA.
  • Sherker AH; National Institute of Diabetes, Digestive and Kidney Disease, National Institutes of Health, Baltimore, MD.
  • Sokol RJ; Pediatric Gastroenterology, Hepatology and Nutrition, University of Colorado School of Medicine, Children's Hospital Colorado, Aurora, CO.
J Pediatr ; 227: 81-86.e4, 2020 12.
Article em En | MEDLINE | ID: mdl-32663593

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Colestase Intra-Hepática / Deficiência de alfa 1-Antitripsina / Hipertensão Portal Tipo de estudo: Clinical_trials / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Newborn Idioma: En Revista: J Pediatr Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Macau

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Colestase Intra-Hepática / Deficiência de alfa 1-Antitripsina / Hipertensão Portal Tipo de estudo: Clinical_trials / Observational_studies / Prognostic_studies / Risk_factors_studies Limite: Adolescent / Adult / Child / Child, preschool / Female / Humans / Infant / Male / Newborn Idioma: En Revista: J Pediatr Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Macau