Atypical Teratoid/Rhabdoid Tumor of the Conus Medullaris.
Pediatr Neurosurg
; 55(4): 215-221, 2020.
Article
em En
| MEDLINE
| ID: mdl-32882703
ABSTRACT
INTRODUCTION:
Atypical teratoid/rhabdoid tumor (AT/RT) is a rare tumor of the central nervous system, especially when involving the spinal column or spinal cord. CASE PRESENTATION We present a case of a 5-year-old girl with progressive bilateral lower extremity pain found to have a discrete nodular lesion of the conus with mild heterogeneous enhancement. Surgical decompression and resection demonstrated a pathologic tumor consistent with AT/RT with loss of INI1 protein on immunohistochemistry. DISCUSSION ANDCONCLUSION:
AT/RT lesions of the conus medullaris are exceedingly rare and associated with extensive disease. We report a rare case of AT/RT with selective involvement of the conus medullaris, as well as describe the surgical, radiographic, and pathologic findings of this tumor.Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Neoplasias da Medula Espinal
/
Neoplasias do Sistema Nervoso Central
/
Tumor Rabdoide
Limite:
Child, preschool
/
Female
/
Humans
Idioma:
En
Revista:
Pediatr Neurosurg
Assunto da revista:
NEUROCIRURGIA
/
PEDIATRIA
Ano de publicação:
2020
Tipo de documento:
Article
País de afiliação:
Estados Unidos