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Improvement of the skeletal phenotype in a mouse model of diastrophic dysplasia after postnatal treatment with N-acetylcysteine.
Paganini, Chiara; Gramegna Tota, Chiara; Monti, Luca; Monti, Ilaria; Maurizi, Antonio; Capulli, Mattia; Bourmaud, Morgane; Teti, Anna; Cohen-Solal, Martine; Villani, Simona; Forlino, Antonella; Superti-Furga, Andrea; Rossi, Antonio.
Afiliação
  • Paganini C; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy.
  • Gramegna Tota C; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy.
  • Monti L; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy.
  • Monti I; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy.
  • Maurizi A; Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, 67100 L'Aquila, Italy.
  • Capulli M; Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, 67100 L'Aquila, Italy.
  • Bourmaud M; Bioscar Inserm U1132 and Université de Paris, Hôpital Lariboisiere, 75010 Paris, France.
  • Teti A; Department of Biotechnological and Applied Clinical Sciences, University of L'Aquila, 67100 L'Aquila, Italy.
  • Cohen-Solal M; Bioscar Inserm U1132 and Université de Paris, Hôpital Lariboisiere, 75010 Paris, France.
  • Villani S; Department of Public Health, Experimental and Forensic Medicine, Unit of Biostatistics and Clinical Epidemiology, University of Pavia, 27100 Pavia, Italy.
  • Forlino A; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy.
  • Superti-Furga A; Division of Genetic Medicine, Lausanne University Hospital and University of Lausanne, 1011 Lausanne, Switzerland.
  • Rossi A; Department of Molecular Medicine, Unit of Biochemistry, University of Pavia, 27100 Pavia, Italy. Electronic address: antrossi@unipv.it.
Biochem Pharmacol ; 185: 114452, 2021 03.
Article em En | MEDLINE | ID: mdl-33545117

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Fenótipo / Acetilcisteína / Densidade Óssea / Modelos Animais de Doenças / Nanismo Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Biochem Pharmacol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Itália

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Fenótipo / Acetilcisteína / Densidade Óssea / Modelos Animais de Doenças / Nanismo Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Biochem Pharmacol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Itália