Bronchiectasis severity correlates with outcome in patients with primary antibody deficiency.
Thorax
; 76(10): 1036-1039, 2021 10.
Article
em En
| MEDLINE
| ID: mdl-33632768
ABSTRACT
Bronchiectasis is a well-recognised complication of primary antibody deficiency (PAD) syndromes. Previous data suggest that mortality in common variable immune deficiency (CVID) is not associated with isolated bronchiectasis. A retrospective analysis of patients with CVID and specific antibody deficiency in two tertiary referral centres with lung disease was conducted. Severity of bronchiectasis at presentation was associated with mortality. Lower FEV1, colonisation with Pseudomonas aeruginosa and a diagnosis of COPD were also associated with mortality. Bronchiectasis is an important driver of mortality in patients with PAD syndromes.
Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Bronquiectasia
/
Imunodeficiência de Variável Comum
/
Doenças da Imunodeficiência Primária
/
Pneumopatias
Tipo de estudo:
Observational_studies
/
Risk_factors_studies
Limite:
Humans
Idioma:
En
Revista:
Thorax
Ano de publicação:
2021
Tipo de documento:
Article
País de afiliação:
Reino Unido