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Intrinsic Defects in B Cell Development and Differentiation, T Cell Exhaustion and Altered Unconventional T Cell Generation Characterize Human Adenosine Deaminase Type 2 Deficiency.
Yap, Jin Yan; Moens, Leen; Lin, Ming-Wei; Kane, Alisa; Kelleher, Anthony; Toong, Catherine; Wu, Kathy H C; Sewell, William A; Phan, Tri Giang; Hollway, Georgina E; Enthoven, Karen; Gray, Paul E; Casas-Martin, Jose; Wouters, Carine; De Somer, Lien; Hershfield, Michael; Bucciol, Giorgia; Delafontaine, Selket; Ma, Cindy S; Tangye, Stuart G; Meyts, Isabelle.
Afiliação
  • Yap JY; Garvan Institute of Medical Research, Darlinghurst, NSW, Australia.
  • Moens L; Clinical Immunogenomics Research Consortium of Australasia (CIRCA), Sydney, NSW, Australia.
  • Lin MW; Department of Microbiology, Immunology and Transplantation, Laboratory for Inborn Errors of Immunity, KU Leuven, Herestraat 49, 3000, Leuven, EU, Belgium.
  • Kane A; Clinical Immunogenomics Research Consortium of Australasia (CIRCA), Sydney, NSW, Australia.
  • Kelleher A; Department of Clinical Immunology and Immunopathology, Westmead Hospital, Westmead, NSW, Australia.
  • Toong C; Faculty of Medicine, University of Sydney, Sydney, Australia.
  • Wu KHC; Garvan Institute of Medical Research, Darlinghurst, NSW, Australia.
  • Sewell WA; Clinical Immunogenomics Research Consortium of Australasia (CIRCA), Sydney, NSW, Australia.
  • Phan TG; Department of Immunology, Liverpool Hospital, Allergy and HIV, Liverpool, Sydney, Australia.
  • Hollway GE; HIV and Immunology Unit, St Vincent's Hospital, Darlinghurst, NSW, Australia.
  • Enthoven K; Faculty of Medicine, St Vincent's Clinical School, Sydney, NSW, Australia.
  • Gray PE; HIV and Immunology Unit, St Vincent's Hospital, Darlinghurst, NSW, Australia.
  • Casas-Martin J; The Kirby Institute for Infection and Immunity in Society, Sydney, Australia.
  • Wouters C; Department of Immunology, Liverpool Hospital, Allergy and HIV, Liverpool, Sydney, Australia.
  • De Somer L; Garvan Institute of Medical Research, Darlinghurst, NSW, Australia.
  • Hershfield M; St Vincent's Clinical Genomics, St Vincent's Hospital Darlinghurst, Darlinghurst, NSW, Australia.
  • Bucciol G; School of Medicine, UNSW Sydney, Sydney, Australia.
  • Delafontaine S; Discipline of Genetic Medicine, University of Sydney, Sydney, Australia.
  • Ma CS; School of Medicine, University of Notre Dame, Fremantle, Australia.
  • Tangye SG; Garvan Institute of Medical Research, Darlinghurst, NSW, Australia.
  • Meyts I; Faculty of Medicine, St Vincent's Clinical School, Sydney, NSW, Australia.
J Clin Immunol ; 41(8): 1915-1935, 2021 11.
Article em En | MEDLINE | ID: mdl-34657246

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Linfócitos B / Linfócitos T / Imunodeficiência Combinada Severa / Agamaglobulinemia Limite: Adolescent / Adult / Aged / Child / Child, preschool / Humans / Infant / Middle aged Idioma: En Revista: J Clin Immunol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Austrália

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Linfócitos B / Linfócitos T / Imunodeficiência Combinada Severa / Agamaglobulinemia Limite: Adolescent / Adult / Aged / Child / Child, preschool / Humans / Infant / Middle aged Idioma: En Revista: J Clin Immunol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Austrália