Pulmonary artery sling: An overview.
Pediatr Pulmonol
; 58(5): 1299-1309, 2023 05.
Article
em En
| MEDLINE
| ID: mdl-36790334
ABSTRACT
Pulmonary artery sling is a rare childhood vascular tracheobronchial compression syndrome that is frequently associated with tracheal stenosis. Consequently, neonates or infants may present with critical airway obstruction if there is long segment airway narrowing and complete rings. Rapid diagnosis of this cardiac vascular malformation and evaluation of the extent and severity of airway involvement is essential to plan surgery, typically a slide tracheoplasty to relieve critical airway obstruction. Long term outcome can be excellent following surgical repair of the stenosed airway and reimplantation of the left pulmonary artery. In this review we focus on the embryology, diagnostic workup, airway investigations and management for this rare but challenging congenital condition.
Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Obstrução das Vias Respiratórias
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Malformações Vasculares
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Cardiopatias Congênitas
Tipo de estudo:
Etiology_studies
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Observational_studies
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Risk_factors_studies
Limite:
Child
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Humans
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Infant
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Newborn
Idioma:
En
Revista:
Pediatr Pulmonol
Assunto da revista:
PEDIATRIA
Ano de publicação:
2023
Tipo de documento:
Article
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