Pulmonary Hypertension in Developmental Lung Diseases.
Clin Perinatol
; 51(1): 217-235, 2024 03.
Article
em En
| MEDLINE
| ID: mdl-38325943
ABSTRACT
Diverse genetic developmental lung diseases can present in the neonatal period with hypoxemic respiratory failure, often associated with with pulmonary hypertension. Intractable hypoxemia and lack of sustained response to medical management should increase the suspicion of a developmental lung disorder. Genetic diagnosis and lung biopsy are helpful in establishing the diagnosis. Early diagnosis can result in optimizing management and redirecting care if needed. This article reviews normal lung development, various developmental lung disorders that can result from genetic abnormalities at each stage of lung development, their clinical presentation, management, prognosis, and differential diagnoses.
Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Síndrome da Persistência do Padrão de Circulação Fetal
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Insuficiência Respiratória
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Hipertensão Pulmonar
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Pneumopatias
Tipo de estudo:
Diagnostic_studies
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Prognostic_studies
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Screening_studies
Limite:
Humans
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Newborn
Idioma:
En
Revista:
Clin Perinatol
Ano de publicação:
2024
Tipo de documento:
Article