Pityriasis Rubra Pilaris: A Multicentric Case Series of 65 Spanish Patients.
Actas Dermosifiliogr
; 2024 Feb 22.
Article
em En, Es
| MEDLINE
| ID: mdl-38401879
ABSTRACT
INTRODUCTION:
PRP is a rare entity of unknown etiopathogenesis. Lack of management guidelines makes it a challenge for clinicians.OBJECTIVE:
To add our experience to increase evidence about PRP.METHODS:
We performed a retrospective, descriptive and multicentric study of 65 patients with PRP, being the largest European case series of patients with PRP.RESULTS:
PRP was more frequent in male patients with an average age of 51 years, but erythrodermic forms presented in older patients (average age 61 years). Six (75%) paediatric patients and ten (60%) non-erythrodermic adults controlled their disease with topical corticosteroids. On the contrary, 26 (68%) erythrodermic patients required biologic therapy as last and effective therapy line requiring an average of 6.5 months to achieve complete response.CONCLUSION:
Our study showed a statistical difference in terms of outcome and response to treatment between children or patients with limited disease and patients who develop erythroderma.
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MEDLINE
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Es
Revista:
Actas Dermosifiliogr
Ano de publicação:
2024
Tipo de documento:
Article