[Multinodular hepatic angioma: a rare cause of neonatal asystole. A case and review of the literature]. / L'angiome hépatique multinodulaire: cause rare d'asystolie néo-natale. Une observation et revue de la littérature.

ABSTRACT

The clinical findings in a case with a diffuse multinodular type of angioma of the liver are reported. The clinical picture was typical the appearance after the first week of a severe congestive failure mimicking a congenital heart disorder, of the left to right shunt type, with gross hepatomegaly of the "vascular" type with a systolo-diastolic murmur, but with no cutaneous evidence of angioma. The very severe prognosis during the first months of life of patients with this malformation, as illustrated by the 58 deaths out of the 78 cases reported in the literature, indicated ligature of the hepatic artery before the age of one month. The satisfactory outcome (with a nine months follow-up) for this case, as for the three other operated cases in the literature, leads us to conclude that this operation is indicated after a detailed arteriographic examination has been made, and provided that the other anatomical conditions are favourable.