RESUMO
Pulmonary artery aneurysm (PAA) is a rare disease, with a poorly known natural history, complex diagnosis and may evolve with serious complications, such as compression of adjacent anatomical structures. In some cases, the presence of such complications is what determines the symptoms and is the initial manifestation of the disease. This paper aims to report the case of a patient with typical angina, submitted to cardiac catheterization, which showed, among other lesions, severe left main coronary lesion with characteristics that led to the suspicion of extrinsic compression, which was identified as caused by a PAA. The treatment chosen in this case was surgical, reported concurrently with a literature review that guided the medical team in their decision-making. RELEVANCE FOR PATIENTS: Surgical correction of PAA may provide resolution of coronary symptoms in affected individuals.