Detalhe da pesquisa
1.
Genetic dissection of the mitochondrial lipoylation pathway in yeast.
BMC Biol
; 19(1): 14, 2021 01 25.
Artigo
em Inglês
| MEDLINE | ID: mdl-33487163
2.
Impaired Mitochondrial Fatty Acid Synthesis Leads to Neurodegeneration in Mice.
J Neurosci
; 38(45): 9781-9800, 2018 11 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-30266742
3.
Genetic modifications of Mecr reveal a role for mitochondrial 2-enoyl-CoA/ACP reductase in placental development in mice.
Hum Mol Genet
; 26(11): 2104-2117, 2017 06 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-28369354
4.
MECR Mutations Cause Childhood-Onset Dystonia and Optic Atrophy, a Mitochondrial Fatty Acid Synthesis Disorder.
Am J Hum Genet
; 99(6): 1229-1244, 2016 Dec 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-27817865
5.
Peroxisomal Pex11 is a pore-forming protein homologous to TRPM channels.
Biochim Biophys Acta
; 1863(2): 271-83, 2016 Feb.
Artigo
em Inglês
| MEDLINE | ID: mdl-26597702
6.
Mitochondrial fatty acid synthesis, fatty acids and mitochondrial physiology.
Biochim Biophys Acta Mol Cell Biol Lipids
; 1862(1): 39-48, 2017 Jan.
Artigo
em Inglês
| MEDLINE | ID: mdl-27553474
7.
The Human Mitochondrial DNA Depletion Syndrome Gene MPV17 Encodes a Non-selective Channel That Modulates Membrane Potential.
J Biol Chem
; 290(22): 13840-61, 2015 May 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-25861990
8.
Phytol is lethal for Amacr-deficient mice.
Biochim Biophys Acta
; 1851(10): 1394-405, 2015 Oct.
Artigo
em Inglês
| MEDLINE | ID: mdl-26248199
9.
Different opinion on the reported role of Poldip2 and ACSM1 in a mammalian lipoic acid salvage pathway controlling HIF-1 activation.
Proc Natl Acad Sci U S A
; 115(32): E7458-E7459, 2018 08 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-30042217
10.
Peroxisomal membrane channel Pxmp2 in the mammary fat pad is essential for stromal lipid homeostasis and for development of mammary gland epithelium in mice.
Dev Biol
; 391(1): 66-80, 2014 Jul 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-24726525
11.
Role of AMACR (α-methylacyl-CoA racemase) and MFE-1 (peroxisomal multifunctional enzyme-1) in bile acid synthesis in mice.
Biochem J
; 461(1): 125-35, 2014 Jul 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-24735479
12.
Metabolic adaptation allows Amacr-deficient mice to remain symptom-free despite low levels of mature bile acids.
Biochim Biophys Acta
; 1831(8): 1335-43, 2013 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-23680781
13.
Defects in mitochondrial fatty acid synthesis result in failure of multiple aspects of mitochondrial biogenesis in Saccharomyces cerevisiae.
Mol Microbiol
; 90(4): 824-40, 2013 Nov.
Artigo
em Inglês
| MEDLINE | ID: mdl-24102902
14.
Apicoplast and endoplasmic reticulum cooperate in fatty acid biosynthesis in apicomplexan parasite Toxoplasma gondii.
J Biol Chem
; 287(7): 4957-71, 2012 Feb 10.
Artigo
em Inglês
| MEDLINE | ID: mdl-22179608
15.
Transfer of metabolites across the peroxisomal membrane.
Biochim Biophys Acta
; 1822(9): 1374-86, 2012 Sep.
Artigo
em Inglês
| MEDLINE | ID: mdl-22206997
16.
Dietary intake of n-3 long-chain polyunsaturated fatty acids and risk of myocardial infarction in coronary artery disease patients with or without diabetes mellitus: a prospective cohort study.
BMC Med
; 11: 216, 2013 Oct 08.
Artigo
em Inglês
| MEDLINE | ID: mdl-24103380
17.
Peroxisomal multifunctional enzyme type 2 from the fruitfly: dehydrogenase and hydratase act as separate entities, as revealed by structure and kinetics.
Biochem J
; 435(3): 771-81, 2011 May 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-21320074
18.
Mitochondrial 2,4-dienoyl-CoA reductase deficiency in mice results in severe hypoglycemia with stress intolerance and unimpaired ketogenesis.
PLoS Genet
; 5(7): e1000543, 2009 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-19578400
19.
Crystal structure of liganded rat peroxisomal multifunctional enzyme type 1: a flexible molecule with two interconnected active sites.
J Biol Chem
; 285(31): 24089-98, 2010 Jul 30.
Artigo
em Inglês
| MEDLINE | ID: mdl-20463028
20.
Identification of a substrate-binding site in a peroxisomal beta-oxidation enzyme by photoaffinity labeling with a novel palmitoyl derivative.
J Biol Chem
; 285(34): 26315-25, 2010 Aug 20.
Artigo
em Inglês
| MEDLINE | ID: mdl-20566640