Detalhe da pesquisa
1.
Phase 3 Open-Label Clinical Trial of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged 2-5 Years with Cystic Fibrosis and at Least One F508del Allele.
Am J Respir Crit Care Med
; 208(1): 59-67, 2023 07 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-36921081
2.
Evidence for Early Cystic Fibrosis Transmembrane Conductance Regulator Modulator Treatment for Children with Cystic Fibrosis Keeps Growing.
Am J Respir Crit Care Med
; 206(11): 1308-1310, 2022 12 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-35947636
3.
Pulmonary exacerbations and clinical outcomes in a longitudinal cohort of infants and preschool children with cystic fibrosis.
BMC Pulm Med
; 17(1): 188, 2017 Dec 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-29228933
4.
Shifting Landscape of Airway Infection in Early Cystic Fibrosis.
Am J Respir Crit Care Med
; 200(5): 528-529, 2019 Sep 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-30875233
5.
Implementation and outcomes of a quality improvement project to systematically assess the gross motor skills in school-aged children with cystic fibrosis.
Pediatr Pulmonol
; 2024 May 23.
Artigo
em Inglês
| MEDLINE | ID: mdl-38780201
6.
Remote endpoints for clinical trials in cystic fibrosis: Report from the U.S. CF foundation remote endpoints task force.
J Cyst Fibros
; 2024 Feb 29.
Artigo
em Inglês
| MEDLINE | ID: mdl-38429150
7.
Managing cystic fibrosis in children aged 6-11yrs: a critical review of elexacaftor/tezacaftor/ivacaftor combination therapy.
Expert Rev Respir Med
; 17(2): 97-108, 2023 02.
Artigo
em Inglês
| MEDLINE | ID: mdl-36803356
8.
Airway Inflammation in Children with Primary Ciliary Dyskinesia.
Ann Am Thorac Soc
; 20(1): 67-74, 2023 01.
Artigo
em Inglês
| MEDLINE | ID: mdl-35984413
9.
A Pilot Randomized Clinical Trial of Pediatric Cystic Fibrosis Pulmonary Exacerbations Treatment Strategies.
Ann Am Thorac Soc
; 20(12): 1769-1776, 2023 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-37683122
10.
Lessons from the lower airway microbiome in early CF.
Thorax
; 72(12): 1063-1064, 2017 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-28450530
11.
Effects of ivacaftor on systemic inflammation and the plasma proteome in people with CF and G551D.
J Cyst Fibros
; 21(6): 950-958, 2022 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-35440409
12.
Case report: Cystic fibrosis with kwashiorkor: A rare presentation in the era of universal newborn screening.
Front Pediatr
; 10: 1083155, 2022.
Artigo
em Inglês
| MEDLINE | ID: mdl-36683818
13.
Detection of bacterial pathogens using home oropharyngeal swab collection in children with cystic fibrosis.
Pediatr Pulmonol
; 56(7): 2043-2047, 2021 07.
Artigo
em Inglês
| MEDLINE | ID: mdl-33847465
14.
Long-term safety of lumacaftor-ivacaftor in children aged 2-5 years with cystic fibrosis homozygous for the F508del-CFTR mutation: a multicentre, phase 3, open-label, extension study.
Lancet Respir Med
; 9(9): 977-988, 2021 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-33965000
15.
Highlights from the 2019 North American Cystic Fibrosis Conference.
Pediatr Pulmonol
; 55(9): 2225-2232, 2020 09.
Artigo
em Inglês
| MEDLINE | ID: mdl-32573948
16.
Oral antibiotic prescribing patterns for treatment of pulmonary exacerbations in two large pediatric CF centers.
Pediatr Pulmonol
; 55(12): 3400-3406, 2020 12.
Artigo
em Inglês
| MEDLINE | ID: mdl-32970375
17.
Characteristics and outcomes of oral antibiotic treated pulmonary exacerbations in children with cystic fibrosis.
J Cyst Fibros
; 17(6): 760-768, 2018 11.
Artigo
em Inglês
| MEDLINE | ID: mdl-29921503
18.
Sputum induction improves detection of pathogens in children with cystic fibrosis.
Pediatr Pulmonol
; 50(7): 638-46, 2015 Jul.
Artigo
em Inglês
| MEDLINE | ID: mdl-25565628
19.
Advances in the diagnosis and treatment of cystic fibrosis.
Adv Pediatr
; 61(1): 225-43, 2014 Aug.
Artigo
em Inglês
| MEDLINE | ID: mdl-25037130