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Endoplasmic reticulum stress in spinal and bulbar muscular atrophy: a potential target for therapy.
Montague, Karli; Malik, Bilal; Gray, Anna L; La Spada, Albert R; Hanna, Michael G; Szabadkai, Gyorgy; Greensmith, Linda.
Afiliação
  • Montague K; 1 Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK2 MRC Centre for Neuromuscular Diseases, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK.
  • Malik B; 1 Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK2 MRC Centre for Neuromuscular Diseases, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK.
  • Gray AL; 1 Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK2 MRC Centre for Neuromuscular Diseases, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK.
  • La Spada AR; 3 Department of Paediatrics, University of California San Diego, La Jolla, CA 92093, USA4 Department of Cellular & Molecular Medicine and Neurosciences, University of California San Diego, La Jolla, CA 92093, USA5 Division of Biological Sciences, University of California San Diego, La Jolla, CA
  • Hanna MG; 2 MRC Centre for Neuromuscular Diseases, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK9 Department of Molecular Neuroscience, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK.
  • Szabadkai G; 10 Cell and Developmental Biology Department, UCL, Gower Street, London, WC1E 6BT, UK11 Department of Biomedical Sciences, University of Padua and CNR Neuroscience Institute, Padua, Italy.
  • Greensmith L; 1 Sobell Department of Motor Neuroscience and Movement Disorders, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK2 MRC Centre for Neuromuscular Diseases, Institute of Neurology, UCL, Queen Square, London, WC1N 3BG, UK l.greensmith@ucl.ac.uk.
Brain ; 137(Pt 7): 1894-906, 2014 Jul.
Article em En | MEDLINE | ID: mdl-24898351

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transtornos Musculares Atróficos / Estresse do Retículo Endoplasmático Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Brain Ano de publicação: 2014 Tipo de documento: Article País de afiliação: Reino Unido

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transtornos Musculares Atróficos / Estresse do Retículo Endoplasmático Tipo de estudo: Prognostic_studies Limite: Animals Idioma: En Revista: Brain Ano de publicação: 2014 Tipo de documento: Article País de afiliação: Reino Unido