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X-linked Dystonia-Parkinsonism patient cells exhibit altered signaling via nuclear factor-kappa B.
Vaine, Christine A; Shin, David; Liu, Christina; Hendriks, William T; Dhakal, Jyotsna; Shin, Kyle; Sharma, Nutan; Bragg, D Cristopher.
Afiliação
  • Vaine CA; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Shin D; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Liu C; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Hendriks WT; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Dhakal J; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Shin K; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA.
  • Sharma N; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA.
  • Bragg DC; The Collaborative Center for X-linked Dystonia Parkinsonism, Department of Neurology, Massachusetts General Hospital, Charlestown, MA 02129, USA; Harvard Brain Science Initiative, Harvard Medical School, Boston, MA 02114, USA. Electronic address: bragg@helix.mgh.harvard.edu.
Neurobiol Dis ; 100: 108-118, 2017 Apr.
Article em En | MEDLINE | ID: mdl-28017799

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transdução de Sinais / Núcleo Celular / NF-kappa B / Distúrbios Distônicos / Doenças Genéticas Ligadas ao Cromossomo X / Células-Tronco Neurais / Fibroblastos Tipo de estudo: Prognostic_studies Limite: Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Estados Unidos

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Transdução de Sinais / Núcleo Celular / NF-kappa B / Distúrbios Distônicos / Doenças Genéticas Ligadas ao Cromossomo X / Células-Tronco Neurais / Fibroblastos Tipo de estudo: Prognostic_studies Limite: Humans Idioma: En Revista: Neurobiol Dis Assunto da revista: NEUROLOGIA Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Estados Unidos