Dietary Management of the Glycogen Storage Diseases: Evolution of Treatment and Ongoing Controversies.
Adv Nutr
; 11(2): 439-446, 2020 03 01.
Article
em En
| MEDLINE
| ID: mdl-31665208
ABSTRACT
The hepatic glycogen storage diseases (GSDs) are a group of disorders where abnormal storage or release of glycogen leads to potentially life-threatening hypoglycemia and metabolic disturbances. Dietary interventions have markedly improved the outcome for these disorders, from a previously fatal condition to one where people can do well with proper care. This article chronicles the evolution of dietary management and treatment of the hepatic GSDs (types 0, I, III, VI, IX, and XI). We examine historic and current approaches for preventing hypoglycemia associated with GSDs. There is a lack of consensus on the optimal dietary management of GSDs despite decades of research, and the ongoing controversies are discussed.
Palavras-chave
Texto completo:
1
Base de dados:
MEDLINE
Assunto principal:
Doença de Depósito de Glicogênio
Tipo de estudo:
Etiology_studies
/
Guideline
Limite:
Humans
Idioma:
En
Revista:
Adv Nutr
Ano de publicação:
2020
Tipo de documento:
Article
País de afiliação:
Estados Unidos