[Severe secondary sclerosing cholangitis as manifestation of a very rare underlying disease]. / Schwere sekundär sklerosierende Cholangitis als Manifestation einer sehr seltenen Grunderkrankung.
Internist (Berl)
; 62(12): 1349-1353, 2021 Dec.
Article
em De
| MEDLINE
| ID: mdl-34546401
ABSTRACT
Langerhans cell histiocytosis (LCH) is a very rare cause of secondary sclerosing cholangitis. We report the case of a 42-year-old male patient with sclerosing cholangitis and histological evidence of LCH from a bile duct biopsy. Due to rapid disease progression and exhaustion of conservative therapeutic approaches the patient received a liver transplantation. Nearly 2 years after transplantation the patient has a good graft function and no signs of recurrence of the underlying LCH.
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Texto completo:
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Base de dados:
MEDLINE
Assunto principal:
Colangite Esclerosante
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Histiocitose de Células de Langerhans
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Transplante de Fígado
Tipo de estudo:
Diagnostic_studies
Limite:
Adult
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Humans
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Male
Idioma:
De
Revista:
Internist (Berl)
Ano de publicação:
2021
Tipo de documento:
Article