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Glucosamine amends CNS pathology in mucopolysaccharidosis IIIC mouse expressing misfolded HGSNAT.
Pan, Xuefang; Taherzadeh, Mahsa; Bose, Poulomee; Heon-Roberts, Rachel; Nguyen, Annie L A; Xu, TianMeng; Pará, Camila; Yamanaka, Yojiro; Priestman, David A; Platt, Frances M; Khan, Shaukat; Fnu, Nidhi; Tomatsu, Shunji; Morales, Carlos R; Pshezhetsky, Alexey V.
Afiliação
  • Pan X; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Taherzadeh M; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Bose P; Department of Anatomy and Cell Biology, McGill University, Montreal, QC, Canada.
  • Heon-Roberts R; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Nguyen ALA; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Xu T; Department of Anatomy and Cell Biology, McGill University, Montreal, QC, Canada.
  • Pará C; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Yamanaka Y; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Priestman DA; Centre Hospitalier Universitaire Sainte-Justine Research Center, University of Montreal, Montreal, QC, Canada.
  • Platt FM; Goodman Cancer Research Centre, McGill University, Montreal, QC, Canada.
  • Khan S; Department of Pharmacology, University of Oxford, Oxford, UK.
  • Fnu N; Department of Pharmacology, University of Oxford, Oxford, UK.
  • Tomatsu S; Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
  • Morales CR; Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
  • Pshezhetsky AV; Nemours/Alfred I. duPont Hospital for Children, Wilmington, DE.
J Exp Med ; 219(8)2022 08 01.
Article em En | MEDLINE | ID: mdl-35704026

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Mucopolissacaridoses / Mucopolissacaridose III Limite: Animals / Humans Idioma: En Revista: J Exp Med Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Canadá

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Mucopolissacaridoses / Mucopolissacaridose III Limite: Animals / Humans Idioma: En Revista: J Exp Med Ano de publicação: 2022 Tipo de documento: Article País de afiliação: Canadá