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Severe kidney dysfunction in sialidosis mice reveals an essential role for neuraminidase 1 in reabsorption.
Kho, Ikhui; Demina, Ekaterina P; Pan, Xuefang; Londono, Irene; Cairo, Christopher W; Sturiale, Luisa; Palmigiano, Angelo; Messina, Angela; Garozzo, Domenico; Ung, Roth-Visal; Mac-Way, Fabrice; Bonneil, Éric; Thibault, Pierre; Lemaire, Mathieu; Morales, Carlos R; Pshezhetsky, Alexey V.
Afiliação
  • Kho I; CHU Sainte-Justine Research Center, University of Montreal, Montreal, Québec, Canada.
  • Demina EP; Department of Anatomy and Cell Biology, McGill University, Montreal, Québec, Canada.
  • Pan X; CHU Sainte-Justine Research Center, University of Montreal, Montreal, Québec, Canada.
  • Londono I; CHU Sainte-Justine Research Center, University of Montreal, Montreal, Québec, Canada.
  • Cairo CW; CHU Sainte-Justine Research Center, University of Montreal, Montreal, Québec, Canada.
  • Sturiale L; Department of Chemistry, University of Alberta, Edmonton, Alberta, Canada.
  • Palmigiano A; CNR, Institute for Polymers, Composites and Biomaterials, Catania, Italy.
  • Messina A; CNR, Institute for Polymers, Composites and Biomaterials, Catania, Italy.
  • Garozzo D; CNR, Institute for Polymers, Composites and Biomaterials, Catania, Italy.
  • Ung RV; CNR, Institute for Polymers, Composites and Biomaterials, Catania, Italy.
  • Mac-Way F; CHU de Québec Research Center, L'Hôtel-Dieu de Québec Hospital, Faculty and Department of Medicine, University Laval, Québec City, Québec, Canada.
  • Bonneil É; CHU de Québec Research Center, L'Hôtel-Dieu de Québec Hospital, Faculty and Department of Medicine, University Laval, Québec City, Québec, Canada.
  • Thibault P; Institute for Research in Immunology and Cancer, University of Montreal, Montreal, Québec, Canada.
  • Lemaire M; Institute for Research in Immunology and Cancer, University of Montreal, Montreal, Québec, Canada.
  • Morales CR; Division of Nephrology, The Hospital for Sick Kids, Faculty of Medicine, University of Toronto, Ontario, Canada.
  • Pshezhetsky AV; Cell Biology Program, SickKids Research Institute, Toronto, Ontario, Canada.
JCI Insight ; 8(20)2023 Oct 23.
Article em En | MEDLINE | ID: mdl-37698928

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Nefropatias / Mucolipidoses Limite: Animals / Humans Idioma: En Revista: JCI Insight Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Canadá

Texto completo: 1 Base de dados: MEDLINE Assunto principal: Nefropatias / Mucolipidoses Limite: Animals / Humans Idioma: En Revista: JCI Insight Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Canadá