RESUMO
Background: Down syndrome (DS) is associated with a high incidence of ear pathologies and hearing loss. There is a paucity of information on the audiology of people with DS particularly those in special schools in Nigeria. This study aimed to compare pneumatic otoscopy with tympanometry for middle ear screening and pure tone audiometry (PTA) with distortion product otoacoustic emission (DPOAE) for hearing screening in the different age groups of people with people DS. Methodology: People with DS in two special schools for people with intellectual disability in Surulere, Lagos state were selected based on the schools' record and their phenotype. Otoscopy, pneumatic otoscopy, tympanometry, screening PTA and screening DPOAE were performed on the subjects. Results: 52 subjects aged 6 to 36years and an M: F ratio of 1.5:1 were studied. 82.7% of subjects had wax impaction. The prevalence of otitis media with effusion (OME) by pneumatic otoscopy was 57.8% and 40.2% by tympanometry and the same number of subjects performed both tests successfully. Screening PTA and DPOAE were successfully performed on 32.7% and 94.2% of the subjects respectively. Fail rate of 29.4% by PTA and 65.3% by DPOAE were recorded. Conclusion: Regular ear check-up in people with DS is essential for the detection and treatment of ear wax, OME and hearing impairment which is highly prevalent in them. Pneumatic otoscopy is recommended for the detection of OME in all the age groups. Screening PTA and OAE are recommended for adults and children and non-cooperative adults hearing screening respectively.