A neonate with crossed pulmonary arteries: a case report and literature review of 115 cases worldwide.

Malposition of the branch pulmonary arteries (MBPA) is an unusual malformation characterised by anomalous origin of both pulmonary arteries from the main pulmonary trunk. To date, only few cases have been reported. Herein, we present the first case report of a 3-day-old, full-term male neonate with the lesser form of crossed pulmonary arteries in Saudi Arabia detected by echocardiography and confirmed by cardiac CT. Crossed pulmonary arteries is not a rare anomaly, but it is a somewhat underreported anomaly, and their recognition is important because it is usually associated with other CHDs, airway obstruction, extra-cardiac anomalies, and certain genetic syndromes.

Validation of the accuracy of handheld echocardiography for diagnosis of congenital heart disease.

BACKGROUND: Handheld echocardiography (HHE) has been increasingly used for rheumatic heart disease screening and in adult emergency room settings. AIMS: This study aimed to validate the accuracy of HHE in the diagnosis of congenital heart disease (CHD). SETTINGS AND DESIGN METHODOLOGY: This is a prospective study carried out at three pediatric cardiology outpatient clinics in Khartoum, Sudan.All patients with suspected CHD were evaluated by clinical examination followed by HHE, performed using a modified segmental approach. Then, a complete study was performed using a standard echocardiography machine. The results were then compared using appropriate statistical tools. RESULTS: A total of eighty cases were included with the following diagnoses either in isolation or combination: ventricular septal defect (n = 23), atrial septal defect (n = 10), pulmonary stenosis (n = 7), tetralogy of Fallot (n = 7), patent ductus arteriosus (n = 6), atrioventricular septal defect (n = 6), transposition of the great arteries (n = 6), and other diagnoses (n = 15). Agreement between HHE and SE was excellent both for visualizing heart segments (κ =77%-100% with a mean of 92.9%) and for diagnosis of CHD (κ =66%-100% with a mean of 91.7%). The sensitivity of HHE was 69.2%-100% (mean = 90.2%) and specificity was 98.5%-100% (mean = 99.3%). CONCLUSION: This study supports extending the utility of HHE in children for screening of CHD in addition to its current role in rheumatic heart disease screening.

Handheld echocardiography for screening and control of rheumatic heart disease study in Gezira state, Sudan: a double approach model.

BACKGROUND: Rheumatic heart disease (RHD) is prevalent in Sudan's rural areas including Gezira state in central Sudan. We initiated a control program aiming at measurement of the echocardiographic (echo) prevalence of RHD, training of health workers and public awareness. METHODS: This is a cross-sectional and interventional study conducted in Gezira State, Al Managil Locality from Nov 2016 to February 2018. We used handheld echo (HHE) to detect the prevalence of RHD in school children and those tested positives were referred for standard echo. In addition, training on detection of RHD for health professionals was offered using training modules for physicians and nurses. Evaluation of health facilities was carried out using a questionaire. This was coupled with educational sessions to increase public awareness about RHD using posters and pamphlets. RESULTS: Two thousand and one hundred twenty-nine school children were screened, 36 cases were positive by HHE, out of these 31 underwent standard echo and 5 were confirmed to have RHD, giving an echo prevalence of 2.3/1,000. All cases had mild mitral regurgitation. Knowledge, attitudes and practices of 175 health workers were assessed then a tailored training program was implemented. Practices that are not compatible with Sudan's RHD Guidelines were detected including performing skin testing prior to administration of benzathine penicillin and under-utilization of local anesthetic to decrease the pain when giving the injection. Benzathine penicillin was available in only 32% of health facilities and only 25% of their personnel received training in RHD management. CONCLUSIONS: RHD echo prevalence in Gezira is relatively high and the health system needs to be strengthened. A double approach, screen-to-control program that utilizes HHE screening, health workers' training, public awareness and providing medical supplies in primary health care centers is feasible.

Echocardiographic screening for rheumatic heart disease in 4 515 Sudanese school children: marked disparity between two communities.

INTRODUCTION: Echocardiographic (echo) screening has unmasked a high prevalence of subclinical rheumatic heart disease (RHD) in many countries, and it can be used as a surveillance tool to control the disease. METHODS: School children of 10 to 15 years of age were selected in two areas of Sudan, Khartoum, the capital, and Niyala in western Sudan. Echo screening using a hand-held echo (HHE) was conducted in Khartoum using a three-view protocol, and in Niyala, a one-view protocol, both modified from the World Heart Federation protocol. Suspected cases were referred for standard echo study. Training of health personnel was conducted and health education sessions were delivered to the public. RESULTS: In Khartoum, a total of 3 000 school children were screened; seven cases were positive for RHD using HHE and one case was confirmed by standard echocardiography. The prevalence of RHD using echocardiography was 0.3 per 1 000 children. In Niyala, a total of 1 515 school children were screened. Using HHE, 59 cases were positive for RHD; 44 had definite and 15 borderline disease. Out of 34 who underwent standard echocardiography, 29 (85.2%) were found to have RHD; 22 had definite and seven borderline disease. The prevalence using echocardiography was 19 per 1 000 children. A total of 779 health workers were trained in South Darfur and 50 000 posters and pamphlets were distributed. CONCLUSION: Using echocardiography, there was a significant disparity in RHD prevalence between the two communities in Sudan. Efforts to control RHD should be directed to this area, and other rural communities should be investigated.