1.
Int J Dermatol
; 62(12): e633-e635, 2023 Dec.
Artigo
em Inglês
| MEDLINE
| ID: mdl-37271828
2.
Am J Dermatopathol
; 40(5): 337-341, 2018 May.
Artigo
em Inglês
| MEDLINE
| ID: mdl-28953013
RESUMO
Light chain deposition disease (LCDD) is a rare systemic disorder with deposition of mostly monoclonal amorphous nonamyloid light chains in multiple organs. Renal involvement with rapidly progressing renal failure presents the dominant manifestation of LCDD. Approximately 20%-30% of patients show symptomatic cardiac or liver involvement. Cutaneous manifestations are extremely rare with only a few published cases. We report 2 additional cases of cutaneous LCDD without detectable systemic disease.