1.
Ann Plast Surg
; 90(6): 631-635, 2023 06 01.
Artigo
em Inglês
| MEDLINE
| ID: mdl-37115944
RESUMO
ABSTRACT: Stiff skin syndrome (SSS) is a rare cutaneous disorder characterized by cutaneous fibrosis resulting in the early onset of thickened and indurated skin, joint mobility restrictions, and contractures. We describe a father and son with familial SSS who presented with bilateral exertional pain and a confirmed diagnosis of chronic exertional compartment syndrome on 4-compartment pressure testing. Patients experienced restored functionality with bilateral 4-compartment fasciotomy. Chronic exertional compartment syndrome should be considered in the differential diagnosis of patients with SSS and chronic pain of the lower limbs.
Assuntos
Síndromes Compartimentais , Contratura , Humanos , Masculino , Fasciotomia/métodos , Síndrome Compartimental Crônica do Esforço , Núcleo Familiar , Doença Crônica , Contratura/genética , Contratura/cirurgia , Pai , Síndromes Compartimentais/etiologia , Síndromes Compartimentais/cirurgia
2.
J Cutan Pathol
; 50(2): 97-100, 2023 02.
Artigo
em Inglês
| MEDLINE
| ID: mdl-35811482