1.
J Neuropsychiatry Clin Neurosci
; 34(4): 307-315, 2022.
Artigo
em Inglês
| MEDLINE
| ID: mdl-36239480
2.
Neurology
; 99(8): 336-337, 2022 08 23.
Artigo
em Inglês
| MEDLINE
| ID: mdl-35705504
3.
J Clin Rheumatol
; 28(3): e672-e674, 2022 Apr 01.
Artigo
em Inglês
| MEDLINE
| ID: mdl-35325906
RESUMO
ABSTRACT: A 65-year-old man with no pertinent medical history presented with 1 month of progressive holocephalic positional headaches (worse supine), photophobia, progressive gait instability resulting in multiple falls (ambulatory to walker in only 2 months), and weight loss. Testing found positive ANCA 1:160 perinuclear patter, myeloperoxidase >8.0. Cerebrospinal fluid found lymphocytic pleocytosis. We present his neuroimaging of isolated hypertrophic pachymeningitis with clinicoradiographic resolution after immunomodulatory pharmacotherapy along with histology from his meningeal biopsy. Isolated vasculitic myeloperoxidase-antineutrophil cytoplasmic antibody hypertrophic pachymeningitis is quite rare.