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Ophthalmic Surg Lasers Imaging Retina ; 54(5): 297-300, 2023 05.
Artigo em Inglês | MEDLINE | ID: mdl-37022313

RESUMO

In this case report, we describe a 34-year-old male patient who presented with vision loss and was found to have profound occlusive retinal vasculopathy. His initial laboratory studies were unremarkable, but five weeks after his ocular symptoms began, he developed acute multi-organ failure and was ultimately diagnosed with atypical hemolytic uremic syndrome (aHUS). His course was complicated by a stroke, respiratory distress requiring intubation, long-term hemodialysis, and eventually death. Occlusive retinal vasculopathy may be the presenting finding in aHUS, although thrombotic microangiopathy syndromes typically present with acute kidney injury and or failure, hemolytic anemia, and thrombocytopenia. [Ophthalmic Surg Lasers Imaging Retina 2023;54:297-300.].


Assuntos
Síndrome Hemolítico-Urêmica Atípica , Microangiopatias Trombóticas , Vitreorretinopatia Proliferativa , Masculino , Humanos , Adulto , Síndrome Hemolítico-Urêmica Atípica/complicações , Síndrome Hemolítico-Urêmica Atípica/diagnóstico , Microangiopatias Trombóticas/complicações , Microangiopatias Trombóticas/diagnóstico , Diálise Renal/efeitos adversos , Diagnóstico Diferencial , Vitreorretinopatia Proliferativa/diagnóstico
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