1.
Lupus
; 13(2): 139-41, 2004.
Artigo
em Inglês
| MEDLINE
| ID: mdl-14995009
RESUMO
We describe the case of a female patient with hereditary complete C4 deficiency and systemic lupus erythematosus. She had suffered from lupus nephritis in early childhood. At the age of 23 years she developed severe lupus with skin disease and life-threatening cerebral vasculitis. Her cerebral disease was unresponsive to high-dose steroids, intravenous immunoglobulin, fresh frozen plasma and plasma exchange. Improvement was achieved with immunoadsorption in combination with mycophenolate mofetil. The patient made a complete recovery and is maintained in complete remission on mycophenolate and low-dose steroids.
Assuntos
Transtornos Cerebrovasculares/etiologia , Complemento C4/deficiência , Lúpus Eritematoso Sistêmico/complicações , Ácido Micofenólico/análogos & derivados , Vasculite do Sistema Nervoso Central/etiologia , Adulto , Transtornos Cerebrovasculares/terapia , Feminino , Humanos , Nefrite Lúpica/complicações , Ácido Micofenólico/uso terapêutico , Prednisolona/uso terapêutico , Vasculite do Sistema Nervoso Central/terapia
2.
Minerva Nefrol
; 29(1): 43-7, 1982.
Artigo
em Italiano
| MEDLINE
| ID: mdl-7099483
3.
Radiol Med
; 66(10): 762-3, 1980 Oct.
Artigo
em Italiano
| MEDLINE
| ID: mdl-6452655