RESUMO
Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive, cutaneous, malignant tumor characterized by high propensity for local relapse and low metastatic potential. It is seen mainly in the age group of 6-65 years over the trunk and extremities. Immunohistochemically it diagnosed by marker human progenitor cell Ag CD 34. Herein, we present a 40-year-old male with DFSP over the pubic area and extending up to the proximal penile shaft. The biopsy revealed intervening bundles of spindle-shaped cells in the dermis and the diagnostic marker human progenitor cell Ag CD 34 was positive. The patient underwent wide local surgical resection.
RESUMO
Lymphoedema-distichiasis syndrome, a type of familial lymphoedema praecox, is a rare, primary lymphoedema of pubertal onset associated with distichiasis and other associations including congenital heart disease, ptosis, varicose veins, cleft palate, and spinal extradural cysts. We report a case of familial lymphoedema with associated distichiasis, atrial septal defect, varicose veins, and recurrent abortions in a 29-year-old female.