Assuntos
Ressecção Endoscópica de Mucosa/métodos , Endossonografia/métodos , Neoplasias Esofágicas/cirurgia , Refluxo Gastroesofágico/diagnóstico , Biópsia por Agulha , Cisto Broncogênico/diagnóstico por imagem , Cisto Broncogênico/patologia , Cisto Broncogênico/cirurgia , Diagnóstico Diferencial , Neoplasias Esofágicas/diagnóstico por imagem , Neoplasias Esofágicas/patologia , Feminino , Humanos , Imuno-Histoquímica , Pessoa de Meia-Idade , Doenças Raras , Medição de Risco , Resultado do TratamentoRESUMO
The pancreatitis, panniculitis and polyarthritis (PPP) syndrome is a rare condition caused by pancreatic diseases, such as acute or chronic pancreatitis or pancreatic carcinoma. We report the first case of PPP syndrome caused by metastatic acinar cell carcinoma from an ectopic pancreas. The symptoms were successfully managed by the treatment of the metastatic carcinoma. Pancreatic cytosteatonecrosis should be always considered in a patient who is showing symptoms of panniculitis and polyarthritis.
Assuntos
Carcinoma de Células Acinares/complicações , Coristoma/complicações , Duodenopatias/complicações , Pâncreas , Neoplasias Pancreáticas/complicações , Idoso , Artrite/etiologia , Carcinoma de Células Acinares/secundário , Humanos , Masculino , Pancreatite/etiologia , Paniculite/etiologia , SíndromeRESUMO
Oral manifestations of severe secondary hyperparathyroidism include maxillary and mandibular deformities, brown tumors, dental abnormalities, and metastatic calcification of soft tissues. We report on a chronic hemodialysis (HD) woman with severe, uncontrolled secondary hyperparathyroidism and a painful, nontender mass in the floor of her mouth. The most likely clinical diagnosis was a bone tumoral lesion of the oral cavity, secondary to renal osteodystrophy. Unexpectedly, pathological examination showed characteristic features of ossifying fibroma (OF) of the jaw, a rare, benign fibroosseous lesion characterized by the replacement of normal bone by collagen and fibroblasts containing varying amounts of mineralized substance. The occurrence of an OF in chronic HD patients is exceptional. Differential diagnosis must be made with bone tumoral lesions secondary to renal osteodystrophy. Surgical removal is the treatment of choice. The pathogenesis of OF in the setting of secondary hyperparathyroidism remains unknown. Parathyroidectomy may not be necessary to avoid OF recurrence after surgical removal.