1.
J Neuromuscul Dis
; 4(1): 17-23, 2017.
Artigo
em Inglês
| MEDLINE
| ID: mdl-28269790
RESUMO
Duchenne muscular dystrophy (DMD) is an inherited myogenic disorder due to mutations in the dystrophin gene on chromosome Xp21.1. The clinical picture included peripheral muscle weakness, cardiomyopathy and chronic respiratory insufficiency. In this paper, the authors review cardiac involvement in patients with DMD, propose a cardiac impairment classification and discuss therapeutic management options.