RESUMO
Trigonocephaly has been described either as an isolated anomaly or as part of the clinical spectrum of some well-known syndromes. Treatment, complications, and prognosis are closely related to the manifestations of the associated anomalies. We report on the main types of syndromes with trigonocephaly and the management of this condition.
Assuntos
Anormalidades Múltiplas , Suturas Cranianas/anormalidades , Craniossinostoses , Craniossinostoses/cirurgia , Humanos , Recém-Nascido , Prognóstico , SíndromeRESUMO
We describe a Brazilian child born with the hypoglossia-hypodactyly syndrome, complicated by bands joining the maxilla to the mandible. Clinical findings are presented, along with the surgical repair procedure.
Assuntos
Anormalidades Múltiplas , Anormalidades Maxilomandibulares/cirurgia , Língua/anormalidades , Displasia Ectodérmica , Humanos , Lactente , Deformidades Congênitas dos Membros , MasculinoRESUMO
This article describes a 20-year-old man with widespread polyostotic fibrous dysplasia that resulted in massive craniofacial deformity with unilateral exorbitism and oronasal obstruction. The patient illustrates the rare occurrence of fibrous dysplasia with major malformation of the face and skull, requiring multiple stages of surgical "sculpture" to improve function and appearance. The disease entity, differential diagnosis, and treatment are discussed.
Assuntos
Ossos Faciais/cirurgia , Displasia Fibrosa Óssea/diagnóstico , Adolescente , Adulto , Idoso , Criança , Pré-Escolar , Ossos Faciais/diagnóstico por imagem , Ossos Faciais/patologia , Displasia Fibrosa Óssea/patologia , Displasia Fibrosa Óssea/cirurgia , Humanos , Lactente , Masculino , Pessoa de Meia-Idade , RadiografiaRESUMO
A variation of the Biesenberger technique of reduction mammaplasty is presented. The medial and lateral blood supply is preserved in a "cut as you go" technique. The results in 68 widely varying cases have been most satisfactory.